How Ayurveda Helps in Lysosomal Storage Disease

Lysosomal storage disease is a group inherited the metabolic disorder, of more than 50 rare diseases, caused by a deficiency of a specific enzyme (Protein that speeds up the reactions in the body). They mainly affect the lysosome, i.e. a structure of the cells that contain hydrolases, which breaks down some biomolecules such as proteins, carbohydrates, and old cell parts so the body can recycle them. In other words, if the lysosome does not function properly, excess substance for decomposition and recycling will remain in the cells. The synthesis of the lysosomal enzyme is controlled by nuclear genes. When a mutation in these genes occurs, it results in 30 different genetic diseases, collectively called lysosomal storage diseases.

Type of Lysosomal Storage Disease

A genetic defect occurs in lysosomes, called a lysosomal storage disease (LSD). Lysosomal storage disease is also called Leukodystrophy, is a congenital metabolic disorder, caused by a dysfunction of an enzyme The main of LSD is the lack of acid hydrolase. Types of Lysosomal storage disease are Mucopolysaccharidoses (MPS) diseases.

• Fabry disease.
• Gaucher disease.
• Tay-Sachs disease.
• Niemann-Pick disease.
• Pompe disease.

Symptoms of Lysosomal Storage Diseases

• Swollen belly.
• Delay in physical development
• Thin chest
• Facial and other bone deformities
• Puffy cheeks
• Joint stiffness and pain
• Irritability
• Difficulty in
• Fatigue, dizziness, abnormal heart rhythm
• Body aches, fever, and tiredness
• Problems with vision and hearing
• Anemia, nosebleeds, and easy bleeding or bruising
• Swollen abdomen due to enlarged spleen or liver
• Pain, numbness, tingling or burning in the hands and feet
• Diarrhea, constipation

Causes of Lysosomal Storage Diseases

Most lysosomal storage disorders are hereditary, i.e. passed down from parents to their children. What happens, usually a child gets symptoms when inherited genesis from both parents. If a child gets the gene from a single parent, he/she will not show any symptoms.

The faulty genes or mutated gene affects the synthesis of enzymes that break down substances in the cells.

It’s a very rare disease, but some forms are more common in certain races. For example, people of the European continent.

Diagnosis

Finding these diseases early is the main key. This disorder test can be done in babies during pregnancy. If a child with symptoms, blood tests can be done to test the enzyme that is missing.

The doctor might suggest these tests:

• MRI
• Biopsy

Treatments definitely slow down the lysosomal storage disease and improve the health of the patient.

Treatments

Though there is no specific treatment for lysosomal storage diseases, a few treatments can help. In this disease:

• Enzyme replacement therapy
• Substrate reduction therapy.
• Stem cell transplant

Treatments to manage symptoms of the disease include:

• Medicine
• Surgery
• Physical therapy
• Dialysis

Treatments With Ayurveda

Analysis of lysosomal storage disease with an Ayurvedic point of view is an outcome of toxin accumulation in the body. This is due to the diminished metabolic activity of the body at tissue level or gene level. As the Ayurvedic principles, the treatment is aimed at ensuring a proper mobilization of the accumulated morbid metabolic toxins at the tissue level. Simultaneously, with the clearing off the toxins, the rejuvenation of the individual cells of the body begins.

Keeping these Ayurvedic principles in mind, Planet Ayurveda has provided a pack, especially for the treatment of lysosomal storage disease,

Lysosomal Storage Disease Pack Of Planet Ayurveda Consists Of

1. Navkarshik Churna
2. Fenugreek Capsules
3. Punarnava Mandoor Tablets
4. Liver Detox Capsules
5. Ashwagandha Capsules
6. Echinacea Capsules

Herbal Remedies for Lysosomal Storage Disease By Planet Ayurveda

1. Navkarshik Churna

Navkarshik Churan from the house of Planet Ayurveda works on the root cause of the problem by correcting metabolism, correcting synthesis of the lysosomal enzyme, purifies the blood and repair the tissue at the gene level. Navkarshik Churna is one of the best herbal remedies for metabolic disorder, thus a boon for lysosomal storage disease patients because it cleanses the toxins accumulated in the body.

2. Fenugreek Capsules

Fenugreek Capsules of Planet Ayurveda have tremendous health benefits. Fenugreek has the immense quality to regulate vitiated Pitta dosha. Fenugreek is known for maintaining a healthy blood glucose level and triglycerides, thus help in maintaining healthy glucose levels in the patients suffering from lysosomal storage disease.

3. Punarnava Mandoor Tablets

Punarnava Mandoor Tablets of Planet Ayurveda are classical Ayurvedic tablets, that helps to maintain water balance in the body. It is a Natural supplement discussed widely in Ayurveda and is excellent to remove toxins from the body. Punarnava mandoor maintains abdominal organs like renal failure, liver failure, fluid accumulation, fatty liver, and many other problems.

Thus, the intake of Punarnava Mandoor Tablets in lysosomal storage disease is quite beneficial as it removes the toxins.

4. Liver Detox Capsules

Liver Detox Capsules of Planet Ayurveda prepared from amazing herbs are beneficial for maintaining good health and keep the liver healthy by eliminating toxins,  thus it is quite beneficial for the patients of lysosomal storage disease as it is the condition, where lysosome could not work properly. These capsules also give a magical effect on – fatty liver, elevated liver enzymes- SGOT, SGPT, liver cirrhosis, etc.

5. Ashwagandha Capsules

Ashwagandha Capsules are made from pure extract of Withania somnifera. These capsules of Planet Ayurveda are useful in neuropathy, fatigue, loss of weight. It enhances physical as well as mental stamina.

6. Echinacea Capsules

Echinacea capsules are prepared from the pure standardized extract of Andrographis Paniculata. Echinacea supports a healthy immune system by treating all types of infections.  It is widely used in Ayurveda also called “Kalmegh”, means dark cloud.

Echinacea of Planet Ayurveda is an herbal supplement, which possesses, anti-parasitic, anti-biotic and anti-parasitic properties.  It is used to treat various body ailments, like hepatitis, flatulence, gastric disorders, bowel complaints, etc. This product is quite beneficial for lysosomal storage disease.

These all Ayurvedic herbal formulations are prepared by Planet Ayurveda carefully designed by the  MD Ayurveda experts, thus provides natural and effective treatment for the patients of lysosomal storage disease. All the herbs are 100 % natural and will not cause any side effects.

Dosage: Recommended to the patient as their age group and symptoms of the disease by the expert physician.