Glycogen Storage Disorder – Causes, Symptoms and Ayurvedic Treatment

Abstract

Glycogen storage disorder is a rare disorder that is characterized by inability to synthesize the glycogen in the body. This is a metabolic disorder that is caused by the deficiency of the enzyme that affects the glycogen synthesis. This disorder is a genetic disease in which the body is not able to store or break down the complex sugar glycogen properly, typically in muscles or liver cells. It affects the liver, muscles and other areas of the body. Our body’s cells need a steady supply of fuel to work properly and that fuel is known as glucose. Our body gets this fuel from breaking down the food we eat. The body combines the glucose units in complex sugar that is called glycogen. It is stored in the liver and muscle cells. When our body needs extra fuel, it breaks down the glycogen into the glucose units. This process is done with the help of some enzymes in the liver and when a person is born with missing enzymes then this process is not working and the body is not able to store or break down the glycogen units. So in this article we are going to discuss Glycogen storage disorder and its Ayurvedic management.

Etiology/Causes

Glycogen storage disorder is caused by two factors i.e. genetic and acquired.

• Genetic Glycogen storage disorder is caused by the error of metabolism (genetically defective enzymes).
• Acquired Glycogen storage disorder is caused by intoxication with the alkaloid castanospermine.

Clinical features/Signs and Symptoms

The child who is born with this condition may have the following symptoms and the symptoms are usually begun at 3-4 months of age

• Liver enlargement
• Kidney disease
• Low level of glucose level
• Elevated uric acid, lipids and lactate
• Possible seizures caused due to repeated episodes of hypoglycemia
• Affected children have doll-like appearance, thin extremities, short stature and protuberant abdomen

Diagnosis

There is no specific test for diagnosing this disorder. The four symptoms might cause the doctor to diagnose the Glycogen storage disorder and that are

• A low blood glucose level
• An enlarged liver
• Lagging growth
• Abnormal blood tests

Ayurvedic Treatment for Glycogen Storage Disorder

We have wonderful Herbal Products for the Management of Glycogen Storage Disorder. Planet Ayurveda has effective herbs and herbal formulations that are made with the extracts of Potential herbs. This is a manufacturing company that manufactures herbal products from the ancient time tested formulas. It is a GMP certified company and this company offers the following herbal products for Glycogen storage disorder.

1. Kumar kalyan ras
2. Nourish max powder
3. Energoplan syrup
4. Arogyavardhini vati
5. Chanderprabha vati
6. Ashwagandha capsules

Products Description

1. Kumar kalyan ras

This is a classical Ayurvedic formulation. It is a very best herbal remedy for child disorders. It helps in brain development, increases strength of bones, provides energy and boosts immunity. It is formulated with Kumari ras (Aloe vera), shuddha Parada (Purified Mercury), Abhrak bhasma (Mica calx), Swarna bhasma (Gold calx), Mukta bhasma (Pearl calx), etc. This formulation can also be used to relieve the symptoms of fever and chronic cough and cold. This formulation is also very helpful in fighting genetic disorders. It can reduce the lipid profile and also high glucose level.

Dosage: 1 tablet to be chewed twice a day with plain water

2. Nourish Maxx powder

This is a herbal formulation in powder form. This powder provides nourishment to the body. This is a health supplement which is used to provide strength to the muscles and helps in supporting the whole skeletal system. This formulation is made from the ingredients like shatavari (Asparagus racemosus), Ashwagandha (Withania somnifera), Safed Musli (Chlorophytum borivilianum) and Gokshura (Tribulus terrestris). This formulation is free from chemicals, preservatives, colour, etc. It is also useful in the treatment of weakness.

Dosage: ½ tsf twice a day after meals with lukewarm water

3. Energoplan Syrup

This is an herbal medicine of Planet Ayurveda in syrup form. It provides strength and energy to the body. This syrup is made from the herbs such as Jeevanti (Leptadenia reticulata), Amalaki (Emblica officinalis), Ashwagandha (Withania somnifera), Pippali (Piper longum), Shigru (Moringa oleifera), etc. This herbal syrup provides strength to the muscles and digestive organs also. This syrup has cooling, calming and soothing effects. It also protects from various infections.

4. Arogyavardhini vati

This is a classical Ayurvedic formulation in a tablet form. This is an effective herbal formulation for fatty liver. It is useful in clearing the accumulated bile and removing the toxins from the liver. It is made from the herbs such as Triphala (Three myrobalans), Chitrak (Plumbago zeylanica), Katuki (Picrorhiza kurroa), Abhrak bhasma (Mica calx), etc. This formulation is used in the treatment of fever, liver disease, acne, eczema, stomach disorders, etc. It also improves the immune system of our body.

Dosage: 1 tablet to be chewed twice a day

5. Chanderprabha vati

This Ayurvedic formulation is used in the treatment of urinary disorders. This medicine has cold potency. This formulation is prepared from the herbs such as Guggul (Commiphora mukul), Karpoor (Cinnamomum camphora), Ativisha (Aconitum heterophyllum), Haridra (Curcuma longa), Vacha (Acorus calamus), Mustak (Cyperus rotundus), Amalaki (Emblica officinalis), Haritaki (Terminalia chebula), Bibhitaki (Terminalia billerica), etc. This formulation provides strength to the muscles and also to the internal organs.

Dosage: 1 tablet twice a day day with plain water

6. Ashwagandha Capsules

This is a single herbal formulation which is made from the standardized extracts of Ashwagandha (Withania somnifera). Ashwagandha effectively acts as a nerve tonic, enhancing physical and mental stamina. This formulation is a natural rejuvenator that helps in providing the proper nourishment to the tissues particularly muscles and bone. It brings back the strength to the muscles and bones.

Dosage: 1 capsule twice a day day with plain water

Conclusion

At the end we concluded that all the genetic disorders are well managed by Ayurvedic herbs and herbal formulations. We must follow the herbal supplements of Planet Ayurveda for better results.